The electroencephalogram in neonatal maple syrup urine disease: A case report

Satish Agadi, Vernon R. Sutton, Michael M. Quach, James J. Riviello

Research output: Contribution to journalArticlepeer-review

Abstract

Untreated maple syrup urine disease (MSUD) leads to encephalopathy in neonates and causes abnormalities on the electroencephalogram (EEG). A case is presented of MSUD with unique features consisting of a comb-like rhythm before the therapy and its disappearance with therapy is presented. This case illustrates the potential use of the EEG in the identification of this specific cause of a neonatal encephalopathy.

Original languageEnglish (US)
Pages (from-to)64-67
Number of pages4
JournalClinical EEG and Neuroscience
Volume43
Issue number1
DOIs
StatePublished - Jan 2012
Externally publishedYes

Keywords

  • Electroencephalography
  • maple syrup urine disease
  • neonatal disease
  • pediatrics

ASJC Scopus subject areas

  • Neurology
  • Clinical Neurology

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