Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation

Mandeep Singh; Sheharyar K. Merwat; Jeffrey H. Fair; Alexander G. Duarte

doi:10.1016/j.rmcr.2021.101443

Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation

Mandeep Singh, Sheharyar K. Merwat, Jeffrey H. Fair, Alexander G. Duarte

Research output: Contribution to journal › Article › peer-review

Abstract

Short telomere syndrome (STS) is characterized as multiorgan dysfunction presenting with unexplained cytopenias, cryptogenic cirrhosis and pulmonary fibrosis. We present a liver transplant recipient that gradually developed hypoxic respiratory failure attributed to idiopathic pulmonary fibrosis associated telomere disease that culminated in a successful single lung transplantation.

Original language	English (US)
Article number	101443
Journal	Respiratory Medicine Case Reports
Volume	33
DOIs	https://doi.org/10.1016/j.rmcr.2021.101443
State	Published - Jan 2021

Keywords

Chronic respiratory failure
Idiopathic pulmonary fibrosis
Interstitial lung disease
Liver cirrhosis
Liver transplant
Lung transplant
Short telomere syndrome

ASJC Scopus subject areas

Pulmonary and Respiratory Medicine

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10.1016/j.rmcr.2021.101443

Cite this

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title = "Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation",

abstract = "Short telomere syndrome (STS) is characterized as multiorgan dysfunction presenting with unexplained cytopenias, cryptogenic cirrhosis and pulmonary fibrosis. We present a liver transplant recipient that gradually developed hypoxic respiratory failure attributed to idiopathic pulmonary fibrosis associated telomere disease that culminated in a successful single lung transplantation.",

keywords = "Chronic respiratory failure, Idiopathic pulmonary fibrosis, Interstitial lung disease, Liver cirrhosis, Liver transplant, Lung transplant, Short telomere syndrome",

author = "Mandeep Singh and Merwat, {Sheharyar K.} and Fair, {Jeffrey H.} and Duarte, {Alexander G.}",

note = "Publisher Copyright: {\textcopyright} 2021",

year = "2021",

month = jan,

doi = "10.1016/j.rmcr.2021.101443",

language = "English (US)",

volume = "33",

journal = "Respiratory Medicine Case Reports",

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AU - Singh, Mandeep

AU - Merwat, Sheharyar K.

AU - Fair, Jeffrey H.

AU - Duarte, Alexander G.

PY - 2021/1

Y1 - 2021/1

N2 - Short telomere syndrome (STS) is characterized as multiorgan dysfunction presenting with unexplained cytopenias, cryptogenic cirrhosis and pulmonary fibrosis. We present a liver transplant recipient that gradually developed hypoxic respiratory failure attributed to idiopathic pulmonary fibrosis associated telomere disease that culminated in a successful single lung transplantation.

AB - Short telomere syndrome (STS) is characterized as multiorgan dysfunction presenting with unexplained cytopenias, cryptogenic cirrhosis and pulmonary fibrosis. We present a liver transplant recipient that gradually developed hypoxic respiratory failure attributed to idiopathic pulmonary fibrosis associated telomere disease that culminated in a successful single lung transplantation.

KW - Chronic respiratory failure

KW - Idiopathic pulmonary fibrosis

KW - Interstitial lung disease

KW - Liver cirrhosis

KW - Liver transplant

KW - Lung transplant

KW - Short telomere syndrome

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Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation

Abstract

Keywords

ASJC Scopus subject areas

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